四氢蝶呤
四氢生物蝶呤(tetrahydrobiopterin)是一种天然存在的营养素,简写为BH4。是参与5-羟色胺、多巴胺、去甲肾上腺素、肾上腺素、褪黑素、一氧化氮生物合成的酶的重要辅助因子
四氢生物蝶呤缺乏症是一种常染色体遗传性疾病,是迄今得以确认的5000~6000种人类的罕见病之一,四氢生物蝶呤缺乏症通过对新生儿进行疾病筛查,检出高苯丙氨酸血症(HPA)后可得到进一步确诊。BH4缺乏症主要会对人的神经系统造成损害,导致患儿出现智力低下、癫痫等症状。
SCMR-333573 |
5,6,7,8-四氢蝶呤二盐酸盐 |
5,6,7,8-Tetrahydropterin dihydrochloride |
N/A |
SCMR-333559 |
(6R,S)-6-羟甲基-5,6,7,8-四氢蝶呤二盐酸盐 |
(6R,S)-6-Hydroxymethyl-5,6,7,8-tetrahydropterin dihydrochloride |
96563-48-3 |
SCMR-333564 |
(6R,S)-6-甲基-5,6,7,8-四氢蝶呤二盐酸盐 |
(6R,S)-6-Methyl-5,6,7,8-tetrahydropterin dihydrochloride |
N/A |
SCMR-333567 |
6,7-二甲基-5,6,7,8-四氢蝶呤盐酸盐 |
6,7-Dimethyl-5,6,7,8-tetrahydropterin monohydrochloride |
66547-54-4 |
SCMR-333533 |
7-四氢-L-生物蝶呤二盐酸盐 |
7-Tetrahydro-L-biopterin dihydrochloride |
35818-62-3 |
SCMR-333523 |
(6R)-5,6,7,8-四氢-L-生物蝶呤二盐酸盐 |
(6R)-5,6,7,8-Tetrahydro-L-biopterin dihydrochloride |
69056-38-8 |
SCMR-333524 |
(6S)-5,6,7,8-四氢-L-生物喋呤硫酸盐 |
(6S)-5,6,7,8-Tetrahydro-L-biopterin sulfate |
109784-74-9 |
SCMR-333522 |
(6R,S)-5,6,7,8-四氢-L-生物蝶呤二盐酸盐 |
(6R,S)-5,6,7,8-Tetrahydro-L-biopterin dihydrochloride |
17528-72-2 |
SCMR-333525 |
(6R)-5-甲基-5,6,7,8-四氢-L-生物蝶呤二盐酸盐 |
(6R)-5-Methyl-5,6,7,8-tetrahydro-L-biopterin dihydrochloride |
N/A |
SCMR-333527 |
(6R,S)-5,6,7,8-四氢-D-生物蝶呤二盐酸盐 |
(6R,S)-5,6,7,8-Tetrahydro-D-biopterin dihydrochloride |
N/A |
SCMR-333529 |
(6R,S)-5,6,7,8-四氢-D-苏式生物蝶呤二盐酸盐 |
(6R,S)-5,6,7,8-Tetrahydro-D-threo-biopterin dihydrochloride |
N/A |
SCMR-333531 |
6 - ((1R,S) - 羟丙基)蝶呤[(1'R,S)-2'-脱氧生物蝶呤] |
6-((1R,S)-Hydroxypropyl)pterin [(1'R,S)-2'-Deoxybiopterin] |
N/A |